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ʻIke ʻia ka lā Thalassemia World World ma ka lā 8 o Mei ma ka hune o ka honua. He lā hoʻomanaʻo kēlā me kēia makahiki i hoʻolaʻa ʻia no nā mea maʻi thalassemikā a me nā mākua i pau ʻole ka manaʻolana no ke ola a me nā ʻepekema pili āpau i hāʻawi ʻole a me, me kā lākou mau hana a me ko lākou kūpaʻa, i hāʻawi ai i kēia manaʻolana, no kahi lōʻihi, maikaʻi maikaʻi. ke ola, i nā mea maʻi thalassemic. I kēia ʻatikala, e ʻike ʻoe i nā mea āpau e pili ana i ka thalassemia.
ʻO ka poʻomanaʻo ʻo World Thalassemia Day 2018 ʻo 'Thalassemia i hala, kēia manawa a me ka wā e hiki mai ana: Ke kākau nei i ka holomua a me nā pono o ka mea hoʻomanawanui ma ka honua holoʻokoʻa'. Wahi a nā loea, ʻo India ke kapikala thalassemia o ka honua me 40 miliona mau halihali a ʻoi aku ma mua o 1,00,000 thalassemia ʻoihana nui e hana nei i ka hoʻokaʻawale koko i kēlā me kēia mahina.
Me nā hōʻoia olakino pale ʻaʻole ʻo ia ka maʻa ma India, ma mua o 1,00,000 mau maʻi ma waena o India e make ma mua o ko lākou huli ʻana i 20 no ka loaʻa ʻole o ka lāʻau. I kēlā me kēia makahiki, ma kahi o 10,000 mau keiki me ka thalassemia nui i hānau ʻia ma India.
Ma kēia World Thalassemia Day, e kūkākūkā mākou e pili ana i ka thalassemia, nā kumu a me ka mālama ʻana.
He aha ka Thalassemia?
ʻO Thalassemia kahi maʻi koko resesive autosomal i hōʻike ʻia e ka hana maʻamau ʻole o hemoglobin i ke kino. Mālama ia i ka nāwaliwali a me ka luku ʻana i nā hunaola ʻulaʻula, pili i ka hoʻokumu ʻana o hemoglobin i ke kino, a kumu i ka anemia akahai a koʻikoʻi paha. Eia kekahi, alakaʻi ia i nā pilikia ʻē aʻe e like me nā deformities o ka iwi, ka nui o ka hao, nā maʻi maʻi puʻuwai, nā palpitations o ka puʻuwai, nā iwi o nā pāpālina a me ka lae paha, hoʻonui ʻia ke ake, jaundice, spleen hoʻonui ʻia, hoʻolohi ʻia ka wā ʻōpio, a pēlā aku.
Hiki i ka mutation genetic a i ʻole kāpae ʻia ʻana kekahi mau ʻāpana kine ke alakaʻi i ka thalassemia a ʻo kekahi o nā ʻōuli maʻamau ka deformities o ka iwi ma nā wahi he nui, ʻili melemele a mae paha, mimi ʻeleʻele, hoʻolohi lohi a ulu ʻana, luhi nui a luhi paha.
lole maxi no ka nui nui
Eia nō naʻe, ʻaʻohe o kēlā me kēia mau ʻōuli ʻike ʻia, kekahi mau ʻōuli o ka thalassemia e hoʻomohala wale ʻia i nā wā hope o ke kamaliʻi a ʻōpio paha.
Kumu o Thalassemia
Ua hoʻoilina ʻia ʻo Thalassemia mai nā mākua, a hiki paha iā ʻoe ke hoʻomohala i ke keiki liʻiliʻi inā lawe kekahi o kou mau mākua i kēia maʻi. A inā he mau halihali makua nā thalassemia, a laila ʻoi aku ke alo o ke keiki i ka hoʻoili ʻana i kahi ʻano thalassemia.
ʻAʻole hōʻike kahi thalassemia akahai i kekahi mau ʻōuli a no laila hiki ke ʻike ʻole ʻia a hiki i ka hoʻāʻo ʻana o ke koko (helu piha o ke koko, hōʻike CBC). Hiki ke mālama ʻia ka thalassemia liʻiliʻi ma o ke kōpili ʻana o ke koko, nā huamoa huaola B hui, a me ka lāʻau chelation therapy a me ke koko a me ka iwi o ka iwi i mea e mālama ai i ka pae maʻamau o hemoglobin a me nā RBC olakino (nā ʻulaʻula koko).
He aha nā ʻano o Thalassemia?
ʻO nā ʻōuli o kēlā me kēia ʻano thalassemia ʻokoʻa ma nā ʻano o ko lākou ʻano a me ke koʻikoʻi.
1. ʻO Beta Thalassemia
Kū ka beta thalassemia ke hiki ʻole i ke kino ke hoʻohua i ka beta-globin. ʻO kēia ʻano thalassemia he ʻelua subtypes, ʻo ia ka thalassemia nui a me thalassemia intermedia. Manaʻo ʻia ʻo Thalassemia nui ka ʻoi aku ka nui ma mua o ka thalassemia intermedia. Hiki i ka Thalassemia nui ke hoʻoweliweli i ke ola me nā ʻōuli e like me ka fussiness, nā maʻi pinepine, nā makemake maikaʻi ʻole, ka maʻi ʻōhiu a me nā ʻoihana hoʻonui. Koi ʻia ke kahe mau o ke koko no nā mea maʻi nui thalassemia.
Ma ka ʻaoʻao ʻē aʻe, ʻoi aku ka paʻakikī o ka thalassemia intermedia a ulu i ka wā e loli ana i nā geneta beta-globin. ʻAʻole koi nā mea maʻi Thalassemia intermedia i ke kuhi koko maʻamau.
2. ʻO Alpha Thalassemia
Hōʻike ʻia ka alpha thalassemia e ke kino ʻaʻole lawa ka alpha-globin. ʻO nā subtypes o alpha thalassemia pū me hemoglobin H a me nā hydrops fetails. ʻO Hemoglobin H ke kumu o ka ulu nui o nā papalina, ka lae a me ka iwi, ka spleen hoʻonui, malnourishment a me ka jaundice. ʻO Hydrops fetails kahi ʻano thalassemia koʻikoʻi, i kū ma mua o ka hānau ʻana i nā hopena i nā hānau hānau a me ka make ma hope koke o ka hānau ʻana.
3. ʻO Thalassemia Minor
ʻAʻole loaʻa i nā mea maʻi ʻo Thalassemia ʻōpio nā ʻōuli, he ʻē aʻe ma mua o ka anemia liʻiliʻi.
He aha nā hopena o Thalassemia ma ka hāpai ʻana?
Hoʻopili ka Thalassemia i ka ulu ʻana o nā mea hānau i ka wā hāpai a me nā wahine me ka thalassemia e ʻeha pū i nā pilikia momona. ʻO nā kumu pōpilikia i ka wā o ka hāpai ʻana e pili pū me nā makaʻala o nā maʻi, hypothyroidism, diabetes diabetes, nā pilikia puʻuwai, ʻoi aku ka nui o nā transfusions koko a me ka iwi haʻahaʻa.
Pehea e kuhikuhi ai i ka Thalassemia
Hana ʻia kahi hōʻike koko e ʻike pono i ka thalassemia e ka hoʻāʻo ʻana i kahi hāpana koko no ka anemia a i ʻole nā pae maʻamau o hemoglobin. Eia hou, e hana ʻia ke kuhi ma muli o ke ʻano o ka thalassemia a me kona koʻikoʻi.
home remedies no nā lehelehe e poni
Lapaʻau o Thalassemia
Ke hilinaʻi nei ka lāʻau thalassemia i ke ʻano o ka thalassemia a me kona koʻikoʻi. ʻO ke kāpili ʻana i ke koko, hoʻoneʻe i ka iwi iwi, chelusi hao (ka hemo ʻana o ka hao nui mai ke kino me nā lāʻau lapaʻau kūikawā) kekahi o nā ʻano lāʻau.
Pehea e pale ai iā Thalassemia?
ʻAʻole hiki iā ʻoe ke pale aku i ka thalassemia, ʻoiai he maʻi koko ia. Eia nō naʻe, hiki ke hoʻokele ʻia me nā lāʻau āpau no ka maʻi hepitis. Pono ʻoe e ʻai i ka papaʻai kūpono a hoʻoikaika mau. Koi ʻia nā mea maʻi Thalassemia e ʻai i ka momona momona, a me nā papa mea kanu. Pono e hoʻopau i nā meaʻai hao i nā palena palena inā kiʻekiʻe nā pae hao i kou koko. Paipai ʻia nā hana hoʻoikaika iki no ka poʻe me ka thalassemia.
Kaʻana i kēia ʻatikala e hana i ka ʻike!
ʻO nā mea āpau āu e ʻike ai e pili ana i Blueberry